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Supernumerary teeth can be an important sign for early diagnosis of an underlying syndrome, and in some circumstances, may be one of the only presenting features. Dentists are best placed to detect supernumerary teeth and therefore, it is important to understand the syndromes associated with them to aid early diagnosis of any associated syndromes. Craniofacial, ophthalmological and gastro-intestinal findings are just a few of the characteristics that may cause a dentist to suspect an underlying genetic disorder. Although it is not within the scope for dentists to diagnose these rare associated syndromes, early referral to the general medical practitioner may in turn help patients access the interdisciplinary management they may need.
CPD/Clinical Relevance: An awareness of the signs and symptoms of syndromes associated with supernumerary teeth can aid early diagnosis.
Article
Supernumerary teeth are those present in addition to the normal complement of the dentition.1 They can occur in isolation or be associated with systemic features as part of a syndrome. The presence of multiple supernumerary teeth is rare and usually associated with certain underlying developmental disorders/syndromes.2
Although the prevalence of syndromes associated with supernumerary teeth is rare, the consequences of such syndromes if left undetected can be severe. Supernumerary teeth can occasionally be the only, or the first presenting feature of an associated syndrome. Dentists are best placed to detect supernumerary teeth and should be vigilant and up to date in their knowledge of the associated syndromes. In knowing what accompanying systemic signs and symptoms to be aware of in a patient's medical history and examination, this could in turn facilitate earlier referral for the diagnosis and long-term interdisciplinary management of these patients.
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