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Images in clinical paediatrics Paediatrics Today 2013;9(2):219 DOI 10.5457/p2005-114.81 PEDIATRIC PARATESTICULAR RHABDOMYOSARCOMA Amir HALILBAŠIĆ, Nešad HOTIĆ, Edin HUSARIĆ Department of pediatrics University Clinical Center Tuzla Tuzla, Bosnia and Herzegovina Key words: Rhabdomyosarcoma ▪ Paratesticular ▪ Orchiectomy. www.paediatricstoday.com a b c Color version available online. A 13-year old boy was referred with a left sided testicular swelling that had been noticed over the past 2 months. On examination a large tumor was noticed in the left hemiscrotum (Panel A). After admission, radical orchiectomy with high cord ligation and wide excision of surrounding soft tissue of the inguinal canal and scrotum were performed (Panel B). he tumor was 13×7×8 centimeters in size (Panel C). Histopathologic exam conirmed the diagnosis of a spindle-cell subtype of paratesticular embryonal rhabdomyosarcoma, and the resection was complete. CT and MRI scans did not reveal enlarged lymphnodes in the retroperitoneum, pelvis and there were no local or distant metastases. he tumor was staged as IRS Group I (fully resected localized disease). Rhabdomyosarcoma is a highly malignant, small blue cell tumor characterized by muscle diferentiation. It is a rare malignancy in children and adolescents. Prognosis is related to initial tumor resectability, as well as the staging of the disease based on tumor invasiveness, tumor bulk, nodal disease and metastases. Multimodal therapy, with surgery, chemotherapy, and radiotherapy provides the patient with an excellent longterm prognosis. With modern treatment, more than 70% of children and adolescents with this disease are cured. Authors’ contributions: Conception and design: AH, EH; Acquisition, analysis and interpretation of data: NH; Drafting the manuscript: AH, EH.; Revising it critically for important intellectual content: AH, NH. Conlict of interest: he authors declare that they have no conlict of interest. Corresponding author: Amir Halilbašić Department of pediatrics University Clinical Center Tuzla 75000 Tuzla Bosnia and Herzegovina hamir@bih.net.ba Tel.: + 387 61 259 016; Fax.: + 387 35 250 474 Received: December 24, 2012; Accepted: April 1, 2013 Copyright © 2013 by University Clinical Center Tuzla. E-mail for permission to publish: paediatricstoday@ukctuzla.ba 219