Weyers acrofacial dysostosis is a rare type of ectodermal dysplasia syndrome characterized by mild short stature, postaxial polydactyly, dystrophic nails, and dental anomalies (hypodontia, microdontia, taurodontism). In this case report, we present the oral and radiographic findings of a 7-year-old girl consistent with the diagnosis of Weyers acrofacial dysostosis. Through this detailed discussion, we aim to contribute to the literature. Keywords: Oral findings, polydactyly, syndrome, Weyers acrofacial dysostosis Hafif boy kisaligi, postaksiyal polidaktili, distrofik tirnaklar ve dental anomaliler (hipodonti, mikrodonti, taurodontizm) ile karakterize otozomal dominant bir bozukluk olan Weyers akrofasiyal disostozis, ektodermal displazi sendromunun nadir gorulen bir tipidir. Bu olgu raporunda, 7 yasindaki kiz cocugunun Weyers akrofasiyal disostozis tanisi ile ortusen oral ve radyografik bulgulari sunulmustur. Bu ayrintili tartisma sayesinde literature katkida bulunmak amaclanmistir. Anahtar Sozcukler: Agiz bulgulari, polidaktili, sendrom, Weyers akrofasiyal disostozis